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Articles Published Processes
1/14/2026 8:39:29 AM | Browse: 0 | Download: 0
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Received |
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2025-06-27 01:09 |
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Peer-Review Started |
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2025-06-27 01:09 |
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First Decision by Editorial Office Director |
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2025-07-17 10:22 |
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Return for Revision |
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2025-07-17 10:22 |
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Revised |
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2025-07-25 08:18 |
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Publication Fee Transferred |
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Second Decision by Editor |
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2025-11-05 02:42 |
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Second Decision by Editor-in-Chief |
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Final Decision by Editorial Office Director |
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2025-11-05 08:51 |
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Articles in Press |
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2025-11-05 08:51 |
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Edit the Manuscript by Language Editor |
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Typeset the Manuscript |
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2026-01-05 02:47 |
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Publish the Manuscript Online |
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2026-01-14 08:39 |
| ISSN |
2220-3230 (online) |
| Open Access |
This article is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution NonCommercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: https://creativecommons.org/Licenses/by-nc/4.0/ |
| Copyright |
The Author(s) 2025. Published by Baishideng Publishing Group Inc. All rights reserved. |
| Article Reprints |
For details, please visit: http://www.wjgnet.com/bpg/gerinfo/247
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| Permissions |
For details, please visit: http://www.wjgnet.com/bpg/gerinfo/207
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| Publisher |
Baishideng Publishing Group Inc, 7041 Koll Center Parkway, Suite 160, Pleasanton, CA 94566, USA |
| Website |
http://www.wjgnet.com |
| Category |
Anesthesiology |
| Manuscript Type |
Minireviews |
| Article Title |
Perioperative management of pediatric patients with inborn errors of metabolism during liver transplantation
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| Manuscript Source |
Invited Manuscript |
| All Author List |
Susan Paulin, Akila Rajakumar, Jagadeesh Menon, Naresh Shanmugam and Mohamed Rela |
| ORCID |
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| Funding Agency and Grant Number |
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| Corresponding Author |
Akila Rajakumar, FRCA, Head, Department of Liver Transplant Anaesthesia and Intensive Care, Institute of Liver Disease and Transplantation, Rela Institute, 7, CLC Works Road, Chromepet, Chennai 600044, Tamil Nadu, India. drakila.rajakumar@gmail.com |
| Key Words |
Inborn errors of metabolism; Anaesthesia for paediatric liver transplantation; Metabolic crisis; Hyperammonemia in paediatric liver transplantation; Perioperative care in metabolic liver diseases |
| Core Tip |
Most metabolic disorders are liver-based, and liver transplantation (LT) has emerged as an effective cure for a variety of inherited metabolic disorders in the pediatric population. LT has been shown to offer a cure, deter disease progression and provide symptomatic improvement in patients with inherited metabolic disorders. Perioperative management of these children presenting for LT with inborn errors of metabolism (IEM) requires disease specific and patient specific strategies in all aspects right from preoperative assessment, intraoperative and postoperative management compared to those presenting with other indications. Knowledge about the distribution of deficient enzymes, the percentage of enzymes replaced by LT, and the extent of extrahepatic involvement helps anticipate and manage complications in the perioperative period. |
| Publish Date |
2026-01-14 08:39 |
| Citation |
Paulin S, Rajakumar A, Menon J, Shanmugam N, Rela M. Perioperative management of pediatric patients with inborn errors of metabolism during liver transplantation. World J Transplant 2026; 16(1): 111122 |
| URL |
https://www.wjgnet.com/2220-3230/full/v16/i1/111122.htm |
| DOI |
https://dx.doi.org/10.5500/wjt.v16.i1.111122 |
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