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Articles Published Processes
4/7/2015 6:08:00 PM | Browse: 1370 | Download: 1490
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Received |
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2014-08-12 08:25 |
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Peer-Review Started |
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2014-08-12 19:48 |
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To Make the First Decision |
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2014-08-27 19:14 |
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Return for Revision |
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2014-08-29 17:05 |
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Revised |
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2014-10-04 22:16 |
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Second Decision |
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2014-10-21 17:32 |
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Accepted by Journal Editor-in-Chief |
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Accepted by Executive Editor-in-Chief |
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2014-10-21 18:04 |
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Articles in Press |
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2014-10-21 18:14 |
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Publication Fee Transferred |
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Edit the Manuscript by Language Editor |
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Typeset the Manuscript |
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2015-03-19 14:17 |
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Publish the Manuscript Online |
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2015-04-07 17:13 |
| ISSN |
1007-9327 (print) and 2219-2840 (online) |
| Open Access |
This article is an open-access article which was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/ |
| Copyright |
© The Author(s) 2015. Published by Baishideng Publishing Group Inc. All rights reserved.
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| Article Reprints |
For details, please visit: http://www.wjgnet.com/bpg/gerinfo/247
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| Permissions |
For details, please visit: http://www.wjgnet.com/bpg/gerinfo/207
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| Publisher |
Baishideng Publishing Group Inc, 7041 Koll Center Parkway, Suite 160, Pleasanton, CA 94566, USA |
| Website |
http://www.wjgnet.com |
| Category |
Gastroenterology & Hepatology |
| Manuscript Type |
Case Report |
| Article Title |
Urea cycle disorders: A case report of a successful treatment with liver transplant and a literature review
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| Manuscript Source |
Unsolicited Manuscript |
| All Author List |
Francesco Giuseppe Foschi, Maria Cristina Morelli, Sara Savini, Anna Chiara Dall’Aglio, Arianna Lanzi, Matteo Cescon, Giorgio Ercolani, Alessandro Cucchetti, Antonio Daniele Pinna and Giuseppe Francesco Stefanini |
| Funding Agency and Grant Number |
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| Corresponding Author |
Francesco Giuseppe Foschi, MD, U.O. Medicina Interna, Ospedale di Faenza, Viale Stradone n°9, 48018 Faenza, Italy. fg.foschi@ausl.ra.it |
| Key Words |
Urea cycle disorders; Hyperammonemia; Diet; Liver transplantation; Quality of life |
| Core Tip |
Urea cycle disorders (UCDs) include a variety of genetic defects which lead to inefficient urea-synthesis with hyperammonemia. The liver is the main site of urea cycle’s enzymatic activity. Diet has traditionally been the primary therapy; orthotopic liver transplantation (OLT) is often considered as a last resort. This case report presents a 17-year-old girl with UCD who was successfully treated with OLT. Her recovery and a recent literature review support OLT as a primary intervention for UCDs patients to prevent life-threatening acute episodes and chronic mental impairment, with an approximately 90% survival rate and a better quality of life. |
| Publish Date |
2015-04-07 17:13 |
| Citation |
Foschi FG, Morelli MC, Savini S, Dall’Aglio AC, Lanzi A, Cescon M, Ercolani G, Cucchetti A, Pinna AD, Stefanini GF. Urea cycle disorders: A case report of a successful treatment with liver transplant and a literature review. World J Gastroenterol 2015; 21(13): 4063-4068 |
| URL |
http://www.wjgnet.com/1007-9327/full/v21/i13/4063.htm |
| DOI |
http://dx.doi.org/10.3748/wjg.v21.i13.4063 |
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