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Articles Published Processes
9/28/2020 7:42:41 AM | Browse: 1217 | Download: 1483
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Received |
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2020-05-30 17:13 |
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Peer-Review Started |
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2020-05-27 17:45 |
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To Make the First Decision |
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Return for Revision |
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2020-07-29 02:44 |
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Revised |
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2020-08-11 09:42 |
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Second Decision |
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2020-09-16 12:09 |
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Accepted by Journal Editor-in-Chief |
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Accepted by Executive Editor-in-Chief |
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2020-09-17 04:55 |
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Articles in Press |
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2020-09-17 04:55 |
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Publication Fee Transferred |
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Edit the Manuscript by Language Editor |
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Typeset the Manuscript |
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2020-09-22 14:50 |
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Publish the Manuscript Online |
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2020-09-28 07:42 |
ISSN |
1007-9327 (print) and 2219-2840 (online) |
Open Access |
This article is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution NonCommercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/ |
Copyright |
© The Author(s) 2020. Published by Baishideng Publishing Group Inc. All rights reserved. |
Article Reprints |
For details, please visit: http://www.wjgnet.com/bpg/gerinfo/247
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Permissions |
For details, please visit: http://www.wjgnet.com/bpg/gerinfo/207
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Publisher |
Baishideng Publishing Group Inc, 7041 Koll Center Parkway, Suite 160, Pleasanton, CA 94566, USA |
Website |
http://www.wjgnet.com |
Category |
Pediatrics |
Manuscript Type |
Case Report |
Article Title |
Abernethy syndrome in Slovenian children: Five case reports and review of literature
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Manuscript Source |
Invited Manuscript |
All Author List |
Jerneja Peček, Petja Fister and Matjaž Homan |
ORCID |
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Funding Agency and Grant Number |
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Corresponding Author |
Matjaž Homan, MD, PhD, Associate Professor, Doctor, Doctor, Department of Gastroenterology, Hepatology and Nutrition, University Children’s Hospital, Faculty of Medicine, University of Ljubljana, Bohoričeva 20, Ljubljana 1000, Slovenia. matjaz.homan@guest.arnes.si |
Key Words |
Abernethy syndrome; Abernethy malformation; Congenital portosystemic shunt; Liver vascular malformation; Children; Infants |
Core Tip |
Although congenital portosystemic shunts causing Abernethy syndrome are rare, the disease is complex, with the possibility of severe multi-organ complications. Searching for the congenital condition should therefore be included in the extended work-up of a newborn with other congenital, especially vascular malformations, neonatal cholestasis or hypergalactosemia. Furthermore, Abernethy syndrome should also be considered in older children presenting with pulmonary arterial hypertension, hyperammonemia and elevated liver enzymes. Additionally, according to our experience, a congenital portosystemic shunt should be considered in the differential diagnosis of children with unexplained hypoglycaemic episodes, gastrointestinal bleeding and osteoporosis with fat-soluble vitamin deficiency. |
Publish Date |
2020-09-28 07:42 |
Citation |
Peček J, Fister P, Homan M. Abernethy syndrome in Slovenian children: Five case reports and review of literature. World J Gastroenterol 2020; 26(37): 5731-5744 |
URL |
https://www.wjgnet.com/1007-9327/full/v26/i37/5731.htm |
DOI |
https://dx.doi.org/10.3748/wjg.v26.i37.5731 |
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