Category |
Medicine, Research & Experimental |
Manuscript Type |
Case Report |
Article Title |
Long-term survival of a patient with a large adrenal primitive neuroectodermal tumor: A case report
|
Manuscript Source |
Unsolicited Manuscript |
All Author List |
Jun Dai, Hong-Chao He, Xin Huang, Fu-Kang Sun, Yu Zhu and Dan-Feng Xu |
ORCID |
|
Funding Agency and Grant Number |
Funding Agency |
Grant Number |
National Natural Science Foundation of China |
81572621 |
Medical and Technology Intercrossing Research Foundation of Shanghai Jiaotong University |
YG2016QN65 |
|
Corresponding Author |
Fu-Kang Sun, MD, Professor, Department of Urology, Ruijin Hospital, Shanghai Jiaotong University, School of Medicine, No.197, Ruijin Er Road, Shanghai 200025, China. sunfukang6@126.com |
Key Words |
Primitive neuroectodermal tumor; Adrenal gland; Case report |
Core Tip |
Primitive neuroectodermal tumor (PNET), a member of small round blue cell tumors, is very rare and highly malignant. PNET is usually found in the chest wall, retroperitoneal and paravertebral areas, but also reported in atypical regions. According to the location, PNET can be classified as central and peripheral PNETs. PNET originating from adrenal is extremely rare and only a few cases have been reported. Currently, the diagnosis of adrenal PNET is mostly dependent on immunohistochemistry, but its specificity is still controversial. Moreover, the outcome of adrenal PNET is poor, standard treatments have never been established so far, and the efficacy of adjuvant chemotherapy and radiotherapy after operation is still unclear. Herein, we reported a case of adrenal PNET in a female patient, and summarized the clinicopathological characteristics of adrenal PNET on the basis of 16 cases available. |
Publish Date |
2019-01-29 02:00 |
Citation |
Dai J, He HC, Huang X, Sun FK, Zhu Y, Xu DF. Long-term survival of a patient with a large adrenal primitive neuroectodermal tumor: A case report. World J Clin Cases 2019; 7(3): 340-346 |
URL |
https://www.wjgnet.com/2307-8960/full/v7/i3/340.htm |
DOI |
https://dx.doi.org/10.12998/wjcc.v7.i3.340 |