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Articles Published Processes
2/27/2019 4:11:15 AM | Browse: 1107 | Download: 1587
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Received |
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2018-12-12 08:55 |
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Peer-Review Started |
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2018-12-13 01:46 |
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To Make the First Decision |
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2018-12-29 01:01 |
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Return for Revision |
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2018-12-29 01:57 |
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Revised |
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2019-01-02 22:04 |
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Second Decision |
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2019-01-14 09:19 |
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Accepted by Journal Editor-in-Chief |
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Accepted by Executive Editor-in-Chief |
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2019-01-15 01:35 |
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Articles in Press |
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2019-01-15 01:35 |
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Publication Fee Transferred |
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Edit the Manuscript by Language Editor |
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Typeset the Manuscript |
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2019-02-26 07:46 |
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Publish the Manuscript Online |
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2019-02-27 04:11 |
| ISSN |
1007-9327 (print) and 2219-2840 (online) |
| Open Access |
This is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/ |
| Copyright |
© The Author(s) 2019. Published by Baishideng Publishing Group Inc. All rights reserved. |
| Article Reprints |
For details, please visit: http://www.wjgnet.com/bpg/gerinfo/247
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| Permissions |
For details, please visit: http://www.wjgnet.com/bpg/gerinfo/207
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| Publisher |
Baishideng Publishing Group Inc, 7041 Koll Center Parkway, Suite 160, Pleasanton, CA 94566, USA |
| Website |
http://www.wjgnet.com |
| Category |
Gastroenterology & Hepatology |
| Manuscript Type |
Case Report |
| Article Title |
Crohn’s-like acute severe colitis associated with Hermansky-Pudlak syndrome: A case report
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| Manuscript Source |
Unsolicited Manuscript |
| All Author List |
Paul Girot, Catherine Le Berre, Astrid De Maissin, Marie Freyssinet, Caroline Trang-Poisson and Arnaud Bourreille |
| ORCID |
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| Funding Agency and Grant Number |
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| Corresponding Author |
Catherine Le Berre, MD, Doctor, Doctor, Institut des Maladies de l'Appareil Digestif, Department of Gastroenterology and Digestive Oncology, Nantes University Hospital, 1 place Alexis Ricordeau, Nantes Cedex 44093, France. catherine@leberre.org |
| Key Words |
Hermansky-Pudlak syndrome; Acute severe colitis; Infliximab; Azathioprine; Inflammatory bowel disease; Case report |
| Core Tip |
Hermansky-Pudlak syndrome (HPS) is a rare autosomal recessive disorder characterized by oculocutaneous albinism, platelet storage pool deficiency and systemic complications. HPS can be associated with Crohn’s disease (CD)-like gastrointestinal disorders. We present a case of acute severe colitis in an albino woman that led to the diagnosis of HPS. Following bleeding diathesis correction by platelet transfusion, the granulomatous colitis responded dramatically to medical treatment with corticosteroids, azathioprine and infliximab. The fact that this HPS-related granulomatous colitis responded to the same therapeutic approach used in CD suggests that this type of colitis may result from HPS patients’ genetic susceptibility to CD. |
| Publish Date |
2019-02-27 04:11 |
| Citation |
Girot P, Le Berre C, De Maissin A, Freyssinet M, Trang-Poisson C, Bourreille A. Crohn’s-like acute severe colitis associated with Hermansky-Pudlak syndrome: A case report. World J Gastroenterol 2019; 25(8): 1031-1036 |
| URL |
https://www.wjgnet.com/1007-9327/full/v25/i8/1031.htm |
| DOI |
https://dx.doi.org/10.3748/wjg.v25.i8.1031 |
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