ISSN |
1948-9366 (online) |
Open Access |
This is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/ |
Copyright |
© The Author(s) 2019. Published by Baishideng Publishing Group Inc. All rights reserved. |
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Permissions |
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Publisher |
Baishideng Publishing Group Inc, 7041 Koll Center Parkway, Suite 160, Pleasanton, CA 94566, USA |
Website |
http://www.wjgnet.com |
Category |
Gastroenterology & Hepatology |
Manuscript Type |
Case Report |
Article Title |
Doege-Potter syndrome by malignant solitary fibrous tumor of the liver: A case report and review of literature
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Manuscript Source |
Unsolicited Manuscript |
All Author List |
Antonella Delvecchio, Loren Duda, Maria Conticchio, Felicia Fiore, Stefano Lafranceschina, Umberto Riccelli, Antonella Cristofano, Bianca Pascazio, Anna Colagrande, Leonardo Resta and Riccardo Memeo |
ORCID |
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Funding Agency and Grant Number |
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Corresponding Author |
Antonella Delvecchio, MD, Surgeon, Department of Emergency and Organ Transplantation, General Surgery Unit “M. Rubino”, University of Bari, 17 Street Mario Pagano, Ceglie Messapica 70124, Bari, Italy. antodel88@libero.it |
Key Words |
Solitary fibrous tumor; Malignant solitary fibrous tumor of the liver; Mesenchymal tumor; Hepatic tumor; Doege-Potter syndrome; |
Core Tip |
Solitary fibrous tumors (SFTs) are rare mesenchymal tumors first described in 1931 by Klemperer and Rabin. Usually, SFTs are benign, but 10%-20% of them are reported to be malignant with a tendency to metastasize. At present, 22 cases of liver malignant SFTs, including our patient, have been reported in literature. Some cases are associated with a paraneoplastic hypoglycaemia definied as Doege-Potter syndrome. Surgery is the best therapeutic modality and prolongs life, but also improves the clinical characteristics associated with Doege-Potter syndrome if present. Longlife follow-up is recommended. |
Publish Date |
2019-08-26 08:35 |
Citation |
Delvecchio A, Duda L, Conticchio M, Fiore F, Lafranceschina S, Riccelli U, Cristofano A, Pascazio B, Colagrande A, Resta L, Memeo R. Doege-Potter syndrome by malignant solitary fibrous tumor of the liver: A case report and review of literature. World J Gastrointest Surg 2019; 11(8): 348-357 |
URL |
https://www.wjgnet.com/1948-9366/full/v11/i8/348.htm |
DOI |
https://dx.doi.org/10.4240/wjgs.v11.i8.348 |