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Articles Published Processes
4/29/2021 8:35:47 AM | Browse: 646 | Download: 1410
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Received |
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2021-01-12 16:17 |
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Peer-Review Started |
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2021-01-12 16:18 |
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To Make the First Decision |
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Return for Revision |
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2021-02-16 06:19 |
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Revised |
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2021-02-28 09:02 |
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Second Decision |
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2021-03-16 12:15 |
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Accepted by Journal Editor-in-Chief |
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Accepted by Executive Editor-in-Chief |
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2021-03-17 05:55 |
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Articles in Press |
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2021-03-17 05:55 |
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Publication Fee Transferred |
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Edit the Manuscript by Language Editor |
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2021-03-23 22:56 |
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Typeset the Manuscript |
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2021-04-25 04:28 |
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Publish the Manuscript Online |
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2021-04-29 08:35 |
| ISSN |
2307-8960 (online) |
| Open Access |
This article is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution NonCommercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/Licenses/by-nc/4.0/ |
| Copyright |
© The Author(s) 2021. Published by Baishideng Publishing Group Inc. All rights reserved. |
| Article Reprints |
For details, please visit: http://www.wjgnet.com/bpg/gerinfo/247
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| Permissions |
For details, please visit: http://www.wjgnet.com/bpg/gerinfo/207
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| Publisher |
Baishideng Publishing Group Inc, 7041 Koll Center Parkway, Suite 160, Pleasanton, CA 94566, USA |
| Website |
http://www.wjgnet.com |
| Category |
Genetics & Heredity |
| Manuscript Type |
Retrospective Study |
| Article Title |
Pediatric Wilson disease presenting as acute liver failure: Prognostic indices
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| Manuscript Source |
Unsolicited Manuscript |
| All Author List |
Wei-Yuan Fang, Kuerbanjiang Abuduxikuer, Peng Shi, Yi-Ling Qiu, Jing Zhao, Yu-Chuan Li, Xue-Yuan Zhang, Neng-Li Wang, Xin-Bao Xie, Yi Lu, A S Knisely and Jian-She Wang |
| ORCID |
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| Funding Agency and Grant Number |
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| Corresponding Author |
Yi Lu, MD, Associate Chief Physician, Center for Pediatric Liver Diseases, Children's Hospital of Fudan University, No. 399 Wanyuan Road, Shanghai 201102, China. luyi@fudan.edu.cn |
| Key Words |
Acute liver failure; ATP7B; D-penicillamine; Liver transplant; Wilson disease; Zinc |
| Core Tip |
This study determined outcomes among 41 recently seen pediatric patients with well-documented Wilson disease (WD) with acute liver failure (ALF) (WDALF) (most confirmed genetically, Wilson disease presenting as acute liver failure) and assessed mortality-model performances. Mortality is low, showing that WDALF children, including those with milder encephalopathy, can survive and recover without Liver transplant (LT) when given D-penicillamine and zinc-salt therapy with or without plasmapheresis. Sensitivity of 7 different prognostic scoring systems was good in our patients but without optimal positive predictive values, indicating that pediatric WD with higher prognostic scores may recover from ALF even after listing for LT. |
| Publish Date |
2021-04-29 08:35 |
| Citation |
Fang WY, Abuduxikuer K, Shi P, Qiu YL, Zhao J, Li YC, Zhang XY, Wang NL, Xie XB, Lu Y, Knisely AS, Wang JS. Pediatric Wilson disease presenting as acute liver failure: Prognostic indices. World J Clin Cases 2021; 9(14): 3273-3286 |
| URL |
https://www.wjgnet.com/2307-8960/full/v9/i14/3273.htm |
| DOI |
https://dx.doi.org/10.12998/wjcc.v9.i14.3273 |
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