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Articles Published Processes
12/27/2021 5:24:00 AM | Browse: 691 | Download: 1267
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Received |
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2021-05-22 09:49 |
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Peer-Review Started |
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2021-05-22 09:54 |
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First Decision by Editorial Office Director |
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2021-07-27 02:29 |
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Return for Revision |
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2021-07-27 02:29 |
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Revised |
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2021-08-19 17:00 |
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Publication Fee Transferred |
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Second Decision by Editor |
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2021-11-04 03:12 |
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Second Decision by Editor-in-Chief |
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Final Decision by Editorial Office Director |
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2021-11-04 23:08 |
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Articles in Press |
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2021-11-04 23:08 |
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Edit the Manuscript by Language Editor |
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Typeset the Manuscript |
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2021-12-13 08:57 |
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Publish the Manuscript Online |
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2021-12-27 05:24 |
| ISSN |
1948-5182 (online) |
| Open Access |
This article is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution NonCommercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/Licenses/by-nc/4.0/ |
| Copyright |
© The Author(s) 2021. Published by Baishideng Publishing Group Inc. All rights reserved. |
| Article Reprints |
For details, please visit: http://www.wjgnet.com/bpg/gerinfo/247
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| Permissions |
For details, please visit: http://www.wjgnet.com/bpg/gerinfo/207
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| Publisher |
Baishideng Publishing Group Inc, 7041 Koll Center Parkway, Suite 160, Pleasanton, CA 94566, USA |
| Website |
http://www.wjgnet.com |
| Category |
Gastroenterology & Hepatology |
| Manuscript Type |
Minireviews |
| Article Title |
Newer variants of progressive familial intrahepatic cholestasis
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| Manuscript Source |
Invited Manuscript |
| All Author List |
Vignesh Vinayagamoorthy, Anshu Srivastava and Moinak Sen Sarma |
| ORCID |
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| Funding Agency and Grant Number |
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| Corresponding Author |
Anshu Srivastava, MD, Professor, Department of Pediatric Gastroenterology, Sanjay Gandhi Postgraduate Institute of Medical Sciences, Raebareli Road, Lucknow 226014, Uttar Pradesh, India. avanianshu@yahoo.com |
| Key Words |
Progressive familial intrahepatic cholestasis; Tight junction protein; Hepatocellular carcinoma; Biliary diversion; Microvillous inclusion disease |
| Core Tip |
Progressive familial intrahepatic cholestasis (PFIC) manifests with a varying spectrum of clinical features, with some variants progressing rapidly into end stage liver disease. Recently, newer variants of PFIC have been described including PFIC 4 due to tight junction protein 2 (TJP2) mutation, PFIC 5 due to NR1H4 mutation and MYO5B related cholestasis also sometimes known as PFIC 6. TJP2 related PFIC also has a risk of hepatocellular carcinoma. This article describes the pathogenesis and clinical features of the newer variants of PFIC. |
| Publish Date |
2021-12-27 05:24 |
| Citation |
Vinayagamoorthy V, Srivastava A, Sarma MS. Newer variants of progressive familial intrahepatic cholestasis. World J Hepatol 2021; 13(12): 2024-2038 |
| URL |
https://www.wjgnet.com/1948-5182/full/v13/i12/2024.htm |
| DOI |
https://dx.doi.org/10.4254/wjh.v13.i12.2024 |
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